VACTERL ASSOCIATION OF INBORN BIRTH DEFECTS - A SURGEON’S OPINION

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VACTERL association is a set of certain abnormalities in one newborn which include defects of the esophagus, rectum, heart, kidneys, vertebral column and extremities. Research papers devoted to the study of this complex disease are still rare. The majority of researchers insist that the syndrome was composed at least of three components (abnormalities of vertebra, tracheoesophageal fistula and anal atresia) though others believe that the constituents of VACTERL are constant. Treatment of the syndrome is usually restricted by surgeries which are needed to restore the esophagus, anus, eliminate abnormalities of the cardiovascular and excretory system and extremities. The scientific research is devoted to the study of VACTERL, correct interpretation of its components, determination of knowledge weaknesses and description of modern therapeutic approaches intended for the correction of surgical abnormalities included into the syndrome.

作者简介

Yu. Kozlov

Municipal Ivano-Matryona Children’s Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduation

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K. Kovalkov

Children’s Municipal Clinical Hospital No. 5

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D. Chubko

Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection

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P. Baradieva

Municipal Ivano-Matryona Children’s Clinical Hospital

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A. Timofeev

Irkutsk State Medical University

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D. Zvonkov

Irkutsk State Medical University

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G. Us

Municipal Ivano-Matryona Children’s Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduation; Children’s Municipal Clinical Hospital No. 5; Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection

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N. Kuznetsova

Municipal Ivano-Matryona Children’s Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduation; Children’s Municipal Clinical Hospital No. 5; Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection

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参考

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版权所有 © Kozlov Y.A., Kovalkov K.A., Chubko D.M., Baradieva P.Z., Timofeev A.D., Zvonkov D.A., Us G.P., Kuznetsova N.N., 2016

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