INFANTILE SOFT TISSUE FIBROSARCOMA OF THE FEMUR IN A 3-MONTH OLD CHILD

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Abstract

Infantile fibrosarcoma (IF) is a rare soft tissue tumor in the pediatric age group. Domestic and foreign literature usually provides single case reports of oncopathology in newborns and infants. A 2-month-old child was examined in a department of surgical oncology of the Scientific and Practical Center for Medical Aid to Children of the Moscow Department of Health who was admitted to the clinic in the end of December of 2013 for examination and treatment for a soft tissue tumor of the right femur. Fibrous soft tissue hamartoma was diagnosed based on the results from medical imaging studies (ultrasound examination, CT angiography) and verification by histology (tumor biopsy). The soft tissue tumor was removed. Histological and immunohistological analysis oftumor tissue confirmed the diagnosis of infantile fibrosarcoma. Radicality of the performed surgical intervention was confirmed microscopically. The child underwent multiagent chemotherapy in the postoperative period. Literature data regarding tumor frequency are provided stating an opinion of oncologists in treatment methods of this rare tumor in newborns and infants.

About the authors

T. A. Sharoev

Scientific and Practical Center for Medical Aid to Children of the Moscow Department of Health

Author for correspondence.
Email: timuronco@mail.ru
Russian Federation

A. V. Sukharev

Scientific and Practical Center for Medical Aid to Children of the Moscow Department of Health

Email: noemail@neicon.ru
Russian Federation

N. M. Ivanova

Scientific and Practical Center for Medical Aid to Children of the Moscow Department of Health

Email: noemail@neicon.ru
Russian Federation

O. V. Klimchuk

Scientific and Practical Center for Medical Aid to Children of the Moscow Department of Health

Email: noemail@neicon.ru
Russian Federation

V. Y. Roschin

Federal Research and Clinical Centre of Pediatric Hematology, Oncology and Immunology of the Ministry of Health of the Russian Federation

Email: noemail@neicon.ru
Russian Federation

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Copyright (c) 2014 Sharoev T.A., Sukharev A.V., Ivanova N.M., Klimchuk O.V., Roschin V.Y.

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