VACTERL ASSOCIATION OF INBORN BIRTH DEFECTS - A SURGEON’S OPINION

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Abstract

VACTERL association is a set of certain abnormalities in one newborn which include defects of the esophagus, rectum, heart, kidneys, vertebral column and extremities. Research papers devoted to the study of this complex disease are still rare. The majority of researchers insist that the syndrome was composed at least of three components (abnormalities of vertebra, tracheoesophageal fistula and anal atresia) though others believe that the constituents of VACTERL are constant. Treatment of the syndrome is usually restricted by surgeries which are needed to restore the esophagus, anus, eliminate abnormalities of the cardiovascular and excretory system and extremities. The scientific research is devoted to the study of VACTERL, correct interpretation of its components, determination of knowledge weaknesses and description of modern therapeutic approaches intended for the correction of surgical abnormalities included into the syndrome.

About the authors

Yu. A. Kozlov

Municipal Ivano-Matryona Children’s Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduation

Author for correspondence.
Email: noemail@neicon.ru
Russian Federation

K. A. Kovalkov

Children’s Municipal Clinical Hospital No. 5

Email: noemail@neicon.ru
Russian Federation

D. M. Chubko

Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection

Email: noemail@neicon.ru
Russian Federation

P. Zh. Baradieva

Municipal Ivano-Matryona Children’s Clinical Hospital

Email: noemail@neicon.ru
Russian Federation

A. D. Timofeev

Irkutsk State Medical University

Email: noemail@neicon.ru
Russian Federation

D. A. Zvonkov

Irkutsk State Medical University

Email: noemail@neicon.ru
Russian Federation

G. P. Us

Municipal Ivano-Matryona Children’s Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduation; Children’s Municipal Clinical Hospital No. 5; Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection

Email: noemail@neicon.ru
Russian Federation

N. N. Kuznetsova

Municipal Ivano-Matryona Children’s Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduation; Children’s Municipal Clinical Hospital No. 5; Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection

Email: noemail@neicon.ru
Russian Federation

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Copyright (c) 2016 Kozlov Y.A., Kovalkov K.A., Chubko D.M., Baradieva P.Z., Timofeev A.D., Zvonkov D.A., Us G.P., Kuznetsova N.N.

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This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.

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